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??????. ???? ????? 36.6  366 ????? ?? ????? ????? ??? ??????? ?? ???????? ?? ???? ????????. ??? ??????? ???? ?????? ?366 ????? ?? ?????? ????? ????? ????? ??????: ????? ????? ????? ??? ????? ??????? ????? ??????? ???? ?????? ???? ??? ???? ???? ??????. ?????? ?????? ???????? ?????? ??????? ??????.

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2. ?????? ????????

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10. ???????

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4. ???????? ????????

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6. ????? ??????? ??????

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9. ?????? ?????? ???????

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10. ???????

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????? 5. ????? ?????? ??????? (???????)


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???? ????? ?? ????? ??? ??????? ???????? ????????????? CTG ?? ??? DMPK ??????? ??? ?????? 19. ?????? ???? ????? ?????. ??? ???? ??????? ?? ??????? ????????? ?? ?? ???? ????? ???? ??? ????? ????? ????????? ???????.

??????? ????? ????? ??????? ????????? ??? ???????? ?????? ?? ?????? ??????? ??? ??????? ??????? ??????.

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2. ?????? ????????

?? ??????? ??????? ????? ?????? ???? ??? ????? ????? ????? ??? ?????? ?????? ??? ?????? ????? ??? ???????? ?? ??????? ????. ??? ??? ?????????? ??????? ?? ????? ??????? ???? ????? ?????? ???????.

?????? ?? ???? ????? ?????? ?? ??????? ??????? ?? ???????? ??? ???? ??????? ??????? ??????? ???????? ??????? ?????. ?????? ???????? ???? ????? ???????? ??????? ????????.

??? ??????? ???????? ??? ????? ????? ????? ????? ????? ?????? ????? ????????? ?????. ??? ????? ????? ????? ????? ??????.

???? ??????? ???? ??????? ???????? ???????? ??????? ?????? ????????? ????? ?????? ???? ????? ??????? ????????? ????????? ?????? ?????? ??????? ??????? ??????.

?? ????? ??????? ?????? ??? ?????? ?????? ?????? ????????? ?????? ????? ?????? ??????. ???????? ??????? ?????? ??????? ??????? ????? ?? ???? ??????? CTG ?? ??? DMPK.


3. ????? ????? ??????? ?????

????? ??????? ?? ?????? ??? ??????? ??????? ?????? ????? ?????? ??? ???? ??????? ??????? ??????? ??? ?????? ????? ?????? ???????????.

??? ??? ????????? ???? ?????? ??? ?????: ????? ?????? ?? ????? ??????? ????????? ????????? ??? ??? ????? ???????? ???????? ?? ?????? ?????? ?? ??? ??????? ??????? ?????? ??????? ??? ??????????? ?? ??????? ??????.

????? ??????? ?????? ????? ???? ?????? ??????? ???????? ?? ????????? ????????? ?????? ?????? ?? ?????? ?????.

??? ?? ????? ????? ????? ??????? ?????? ??????? ???????? ???????? ????? ?????? ??? ??? ??????? ?? ???? ????? ????? ?? ????? ??????? ????????.


4. ???????? ????????

???????? ???????? ?? ??? ??????? ???? ???? ???? ???? ?????? ??? ????? ???????? ??? ????? ?????? ??? ?????? ?? ??? ?????? ????????.

???? ?????? ?????? ??????? ????? ???? ?????? ??????? ???? ??????? ?????? ????????? ???? ??????? ???????? ?????? ????? ???????. ??? ????? ???? ????? ?????? ??????? ???? ?? ???? ????? ????????.

?? ???? ??????? ???????? ?????? ????? ?????????? ??????? ???? ????? ???????. ???? ??????? ??? ??? ?????? ?????? ?? ???????? ???? ????? ?????? ???????.

??????? ??????? ??????? ?????? ??? ????? ????? ??????? ??? ???????? ??????? ??????? ???????. ?????? ???? ?????? ????????? ???? ?????? ????? ?????? ????? ???????? ??? ??????? ???????.

?? ???? ????????? ???????? ???????? ???????? ??????? ?????? ????? ?? ????? ????? ??????? ??????? ????? ????? ???? ?????? ???? ?????? ??? ???? DM1. ??? ???? ?? ???? ???????? ??????? ?????? ?????? ??? ??? ????? ???????? ??? ???? ?? ????? ??? ????? ?????? ?????? ??????? ???? ????? ?????????? ????? ??????.


5. ??????? ??????? ??????? ???????? ???????

????? ??? ??????? ?????? ????? ?????? ??????? ?????? ????? ??????? ????????? ??????. ?????? ?????? ??? ?????? ??? ???????? ????????? ?????? ?????? ??????? ?????? ???????.

???? ??????? ?????? ????? ????? ??? ???? ?????. ??? ????? ???????? ?????????? ?????? ?? ???????? ???????? ???? ??? ???? ???? ???????? ?????? ??????.

???? ??????? ??????? ????????? ??????? ??? ????? (TENS) ?????? ????? ?????? ??? ???? ??????? ?????. ??? ??????? ????????? ?????? ?????? (NMES)? ???? ????? ??????? ???????? ????? ?????? ?? ?? ?????? ???? ????? ??? ??????? ??????? ?? ????? ?????????? ?? ????? ??????? ??????? ?? DM1.

???? ?? ???? ??????? ??? ??????? ???????? ??????? ??????? ??? ??????? ??????? ????????? ??????????? ????? ?????? ???? ?????????? ??? ??? ????. ??????? ????? ????? ??????? ????? ??????? ???????? ?????? ????????? ???????? ?????? ????????.

???? ???? ??? ??? ??? ??????? ????????? ???????? ??? ??????? ??? ?????? ????? ????? ?????? ????? ?? ?????? ????? ?????? ?? ???????? ????? ?? ??? ?????.


6. ????? ??????? ????????

???? ???????? ????????? ?????? ?? ??? ??????? ??????? ?????? ??? ???? ?????? ?? ??? ??????? ????? ????? ????? ?????.

?? ??? ???????? ?????? ????? ????? ?????? ?????? ????? ????? ???????? ??? ????? ????? ????? ???? ?????? ??? ??????.

??? ??? ??????? ???? ??????? ????? ??? ????? ????? ?????? ?????? ????? ?????? ?????? ?????? ??????? ?????? ?????? ???????? ???????.

??? ?? ????? ?????? ??????? ???????? ??? ????? ?????: ??? ?????? ?????? ????? ????? ?????? ?????? ???? ??? ????? ?? ?????? ?????.

??? ???????? ?????? ?? ?????? ??? ??????? ????? ?? ??????? ????? ?????? ?????? ?????? ??????? ?? ?????? ????????.


7. ????? ??????? ??????? ???????

???? ???????? ??????? ?????? ?? ???? ??????? ?? ??? ???????? ??? ???? ??? ????? ???? ????? ?????? ????? ?????.

????? ?????? ??? ?????? ?????? ??? ???? ?????? ??? ?? ??? ????? ????? ?????? ????? (ECG) ??? ????? ?????? ??? ?????. ?????? ??? ????? ?????? ??? ????? ????? ?????? ???? ?????????. ??? ????? ???????? ??????? ?????? ??? ????? ?????.

?? ????? ?????????? ???????? ???? ????? ?????? ??????? ????? ?????? ????? ????? ??????? ?????? ??????.

??? ???????? ???? ???????? ????? ??????? ???????? ??????. ???????? ??????? ??? ??????? ?????? ???????? ??? ?????? ??? ???? ???????.

????? ???????? ????? ????? ??? ????????? ?????? ??????? ??????? ???????? ?????.


8. ????? ????????? ???????

??? ??? ??????? ?????? ??????? ?????? ????? ???????? ??? ????? ??????? ??????? ?????????? ?????? ??????? ??????? ??????.

?? ????? ??? ???????? ??????? ??????? ??? ??????? ?????? ?????? ??????? ???????? ????????? ??????? ?? ???????? ??? ????? ??? ??????? ????????.

????? ???????? ???? ???? ????? ??????? ????? ??? ???? ?????? ???????? ???? ???? ?????????? ?? ????? ?? ????? ????? ??????? ????? ?????.

??? ???? ???????? ?????? ??????? ???? ???????? ?????? ??? ????? ???? ?????? ??? ???? ?? ????? ?????????.

?? ?????? ?????? ?????? ?????? ??? ????????? ???????? ???????? ???????? ????????. ???? ????? ???? ??????? ?????? ?????? ?? DM1 ??? ?? ????? ??????? ??? ????? ???????.


9. ?????? ?????? ?????? ??????

????? ?????? ??????? ??????? ?? ?????? ?????? ???? ?????? ???????. ???? ??? ?????? ????? ?????? ?????? ??????? ????? ?????? ????? ????? ???? ?????.

??? ??????? ??????? ???????? ????????? ????? ?????? ?????? ???? ????? ?????? ?? ??? ????. ???????? ??????? ???? ?? ????? ????? ????? ??????.

????? ?????? ?????? ???????? ??? ??????? ???????? ??????? ??????? ?????? ??????? ????? ????? ?????? ??????? ???????? ?????? ??????.

????? ?????? ????????? ????? ???? ????? ?????? ???? ??????? ???????? ????? ?????? ????????.

?? ??????? ??????? ?????????? ????? ???????? ??????? ??????? ????? ????? ?????? ???????? ????? ?????.


10. ???????

????? ????? ?????? ??????? ???????? ????? ?????? ??? ?????????? ??????? ?????? ?? ??????? ?????? ?? ???? ?????.

?????? ??????? ??????? ?? ??????? ??????? ???????? ?????? ?? ?????? ????? ???????? ?? ?????? ?????? ???????.

??? ????? ?? ????? ??????? ????? ??????? ??? ?????? ??????? ??? ????? ?????? ????????? ????? ??????? ?????? ?????? ????? ?????? ?????? ?????? ??????? ?? ???????? ????? ???????.

????? ?????. ??????? ??????? ????????




????? 6. ????? ?????? ????????????


????? ?????? ????????????


1. ??????? ?????? ?????

????? ?????? ???????????? ??? ???? ???? ????? ????? ????? ??????? ???????? ???????? ??????? ?????? ?????? ??????? ???????? ?????? ?????.

????? ???? ??????? ???????? ??????? ?? ??????? EMD ?LMNA? ?????? ?????? ??? ???????? ????? ?? ?????? ??? ???? ???? ?????? ????????. ????? ????? ????? ?????? ??????? X? ????? ????? ?????? ?????? ????? ?????? ??? ??????. ?????? ???????? GeneReviews? ???? ???? ???????? ???????? ????? ?????? ???????????? ??? 1.32 ???? ??? 100,000 ????. ??? ????? ??????? ??????? X ??? ??? ??????? ?? ???? ??? 0.130.2 ???? ??? 100,000 ???.

?? ???? ??????? ???????? ?? ???????? ??? ???? ????? ???? ??????? ??????? ??? ?????? ????? ???????. ??????? ??? ?????????? ??????? ???????? ??????? ?????? ??? ??? ??????? ???????? ??????? ?????? ????.

??? ????? EDMD ?? ??????? ??????? ??????? ?????? ?? ?????? ???? ??????? ????? ?????.


2. ?????? ????????

???? ??????? ?????? ?? ?????? ????? ????????? ???? ????? ????? ?????? ??? ??????. ????? ??? ?????? ??? ???????? ?????? ?? ??? ??????? ??? ????? ?? ????? ????? ??? ??????.

?????? ?? ???? ????? ?????? ?? ??????? ?????? ????? ?? ??????? ???????? ?????? ???????. ??????? ??? ?????? ?????? ??????. ??? ????? ?????? ????? ???? ????? ????? ?????.

?? ???? ????? ???? ???????? ????? ?????? ???? ????? ?????? ????? ?????? ?????? ??????? ???????.

???? ??????? ??????? ???????? ??????? ????????? ????? ???????? ????????? ??????? ???? ?????. ??? ???? ?????? ???????? ??????? ???? ?????. ????? ??? ??? ?????? ?????? ??? ???? ?? ??? ????? ????? ?????.

????? ??????? ??? ?????? ???????? ??????? ?????? ?????? ??????????? ???????? ????????.


3. ????? ????? ??????? ?????

??? ???? ??????? ???? ???? ???? ????? ?????? ???????? ??????? ????????? ??? ????? ?????? ?? ???????? ????? ?? ??????? ?????? ???????? ?? EDMD.

???? ??????? ????????:

?????? ??? ??? ????? ???????? ??????? ???????? ?????? ???????

?????? ??? ??? ???? ??? ?????? ?????? ???????

??????? ?? ???????? ????? ???????? ???? ????? ?????

?????? ??? ?????? ?????? ?????? ?? ??? ????? ?????

?????? ??? ??????????? ?? ?????? ??????? ?????? ???????? ???????.

??? ??????? ???????? ????? ????? ??????? ?? ?????? ??????? ???????. ?????? ??? ?????? ?????? ??? ????? ????? ????? ????? ???????? ?????.


4. ???????? ????????

???? ???????? ???????? ?? ??? ??????????? ?????? ???? ???????. ????? ?????? ??? ???????? ????? ????? ???? ?????? ????? ???? ??????.

???? ???????? ??????? ???????? ?????? ??? ??? ?????? ??????? ????????. ???????? ???????? ????? ???????? ??? ?????? ??????? ??? ??????? ?????? ??? ??????? ???????? ????????.

??? ??? ????? ????? ??????? ?????? ???? ?????? ?????? ?????? ????? ?????? ????? ?????? ??????? ?? ?????? ?? ???????? ??? ?????. ???? ??? ???? ????? ????? ?? ????? ???????.

??? ????? ???? ??????? ????? ????? ???? ????? ??? ??? ???. ?????? ????? ?????? ??????? ?????? ???? ??????.

??? ??????? ??????? ???? ?? ???? ???????? ????? ?????? ????? ??????? ??????? ????? ?????? ?????. ???? ???? ?????? ?????? ???? ???????? ???????? ?? ????? ???? ??????? ?? ?????? ????? ???????.

????? ???????? ???????? ??? ????? ?????? ??????? ?? EDMD ???????? ?????? ?????? ??????? ?????? ????? ?????? ????? ?????? ?????? ???????.


5. ??????? ??????? ??????? ???????? ???????

???? ??????? ??????? ?? EDMD ?????? ???????? ?????? ???????? ????? ?? ????? ??????? ???????? ?????? ?? ??????? ???? ???????.

??????? ?????? ??????? ?????? ???????? ??? ??????? ??????. ???? ????? ?? ???????? ???????? ???????? ?? ???? ??????? ?????? ?????? ?? ??????? ???????????.

??? ???? ???????? ???? ????? ??????? ??????? ??????? ????????? ??????? ??? ????? (TENS) ?? ?????? ?????? ??????? ??????. ??? ???? ??????? ????????? ?????? ?????? (NMES) ????? ?????? ?????? ????????? ?? ????? ???? ????? ??????? ????? ????? ??????? ???????.

???? ?????? ?????? ??????? ??? ??????? ???????? ??? ??????? ???????? ??? ???? ????????? ????? ??????? ??? ?? ???? ???? ????? ??? ????????? ?? EDMD ???????. ???????? ?????? ????????? ??????????? ???????? ?????.

?????? ???? ?????? ????? ????? ?????? ????? ?? ?????? ????? ?????? ???????? ?????. ??? ???? ????? ??????? ????????? ?????????? ??????????????? ??? ??? ?????? ?? ??????? ?? ?????? ??????? ??????? ??? ?????? ???? ?????.


6. ????? ??????? ????????

???? ??????? ????????? ?? EDMD ??????? ?????? ??? ??????? ?? ???????? ???? ?? ??? ??????? ??????? ????? ????? ??? ?? ???? ????? ??????? ??????.

?? ??????? ???????? ????? ?? ??????? ????? ????? ????? ???? ??????? ???????? ????? ?????? ??? ?????? ??? ??? ?????? ??????.

???? ?????? ??????? ??????? ??? ???? ??? ???? ?? ????? ????. ?????? ?????? ?? ?????? ???? ??????? ?????? ????? ?????? ???????? ??????? ??????? ?? ???? ??????.

????? ?????? ???????? ??????? ??????? ??? ??????? ????? ???? ??????? ???????. ??? ???? ????? ??????? ?? ???????? ???????? ?????? ??? ??????? ????? ??????.

??? ???? ?????? ?????? ?????? ???? ??????? ??? ?????? ??????? ??????? ????? ????? ????? ??????? ??????.

??? ????? ??????? ??????? ?????????? ??? ???????? ?????????.


7. ????? ??????? ??????? ???????

???? ????? ????? ?? EDMD ????? ??????? ???????? ??? ?????? ?????? ?? ??? ????? ??????.

????? ?? GeneReviews? ??? ?? ???? ????? ????? ?????? ????? (ECG) ??????? ????? ?????? ??? ????? ??? ????? ?????? ??? ?????. ???? ?????? ???????? ??????? ?? ?????? ???? ?????? ????? ????? ????????.

????? ??? ?????? ??? ??? ????? ????? ?? ???? ????? ???? ???? ?????. ??? ??? ??????? ????????? ??? ???? ???????? ???? LMNA? ???? ??? ???????? ????? ???????? ??????? ?????? ??? ??? ??? ????? ????? ???????.

???? ??? ?? ????? ???????? ??? ??????? ?????? ??? ????? ???? ?????? ???? ??????? ??????? ???????? ?????.

?? ?????? ??????? ???????? ????? ??? ????? ?????? ???????? ???? ????? ??????. ?????? ???? ??????? ??????? ????? ?????? ?????? ????? ????? ?? ????? ??? ???? ?????? ??? ??? ???? ???????? ???? ????? ???????? ??? ????? ?????? ??? ?????.

??? ???? ???? ?????? ??????? ????? ?????? ????? ???????? ??? ???? ??????? ??? ??????? ????????? ??? ?????? ??? ??????.


8. ????? ????????? ???????

????? ????? ??????? ?? EDMD ???? ????????? ??????? ???????. ??? ????? ????????? ??????? ?????? ????? ????? ???????? ??? ??? ?????? ?? ????? ????? ?? ?????? ??????? ???? ????? ??? ??????? ????? ???????.

??? ??????? ?? ????????? ????? ????????? ???????? ?????? ?????? ???????? ???????? ??????? ?????? ????.

????? ?????? ?????? ?????? ?????? ?????? ????? ????? ??? ??? ?????? ????? ??? ????? ?????? ?????? ?????? ???????.

??? ???? ????? ?? ???? ???? ??????? ?? ??? ???? ?? ??? ??? ??? ?????? ??? ????? ?????? ????? ?????? ????? ??? ????.

??? ?????? ???? ????? ????? ?????? ??? ?????? ????????? ???????? ??? ???????. ????? ????? ????? ???????? ?????? ??????? ??? ???????? ????????.


9. ?????? ?????? ?????? ??????

?? ????? ????? ?? ???????? ?? EDMD ?? ????? ??? ??? ???? ?? ?????? ????? ??????? ????? ??????. ????? ???? ????? ???? ??????? ??????? ??? ??? ?????? ??? ?????? ??? ????? ??????????.

??? ?? ?????? ???????? ???????? ?? ?????? ?????? ??? ????? ?? ??? ????? ?????. ?????? ?????? ??? ?????? ??????? ??????? ??? ??? ???????? ????? ????? ??????.

????? ????? ?????? ??????? ?????? ????? ????? ????? ??? ???? ??????? ??????? ?????? ??????? ?????? ????? ?????.

??? ??? ????? ?????? ??? ?????? ????? ????? ????????. ???????? ???????? ??????? ????????? ??? ?????? ?? ???? ?????? ??????? ?????? ??????? ?????.

???? ????? ?????? ??? ????? ????? ?????? ?????????? ???????? ?????? ??????? ?????? ??? ???? ???????.


10. ???????

????? ????? ?????? ???????????? ??????? ???????? ??????? ?????? ?????? ?? ?????? ?????? ?????? ??????????? ??????? ???? ?? ???? ?????.

?????? ????? ??????? ?????? ??????? ?? ????? ????? ???????? ?? ?????? ??????? ??? ???? ???? ???? ????. ??? ????? ???? ???? ???? ????? ?????? ??????? ??? ?????? ??????.

????? ????? ??????? ??????? ??????? ?????? ??? ??????? ????? ??????? ????? ??????? ????? ?????? ????? ?????? ??? ?????? ??? ???? ??????? ???????? ?? ????????? ??????? ????? ???????? ?????? ???????.




????? ??????. ??????? ???????? ?????? ??????





????? 7. ?????? ?????? ?????? (SMA)


?????? ?????? ?????? (SMA)


1. ??????? ?????? ?????

?????? ?????? ?????? ??? ???? ???? ????? ????? ????? ????????? ??????? ?? ?????? ???????? ????? ??????? ?? ???? ??? ??????? ??????? ????????.

????? ?????? ?????? ?? ?????? ?????? ?????? ??????? ???????? 5q? ????? ?? ?????? ?????? ?? ???? ????? ??? SMN1 ??????? ??? ?????? ??????. ????? ??? ??????? ?? ?????? ?????? ???????. ?????? ??? SMN2 ?????? ??? ?????? SMN? ????? ??? ???? ?? ??? ?????? ???? ?? ???? ??????? ?????? ?????? ??? ?? ????.

????? ???????? ?????? ??????? ???? ???? ????? ??????? ???????? ??????? ?????? ?????? ?? ??? 5q ??? ???? ????? ??? 6,00012,000 ????? ??? ??? ????? ???????? ??????? ?????? ?????????.

????????? ??????? ???? ????? ??????? ?? ????? ?????? ??????? (????? 0) ??? ????? ???? ???? ?? ?? ?????? (????? IV). ??? ???????? ??????? ????????? ????? ????? ???? ????? ???????? ????? ????? ????? ?????? ??????? ??????? ?????? ??? ??????? ?????? ???????.


2. ?????? ????????

?????? ??????? ?????? ?????? ?????? ?? ??? ???? ??????? ???? ???? ??? ?? ??????? ??????? ?? ???????. ??? ?????? ??????? ?????? ???? ??????? ???? ????????? ??????? ???????? ?????? ??????.

?? ????? ????? ?? ?????? ?? ????? ????? ?????? ??? ?????? ??????? ??? ????? ????? ?????? ???? ??? ???? ???? ???? ??????? ??????? ????????? ??????.

?? ????? ??????? ?????? ?????? ?????? ???????? ???? ?? ????? ???? ?????? ??? ????? ???????. ??????? ?? ????? ????? ????????? ???????? ??????? ????? ??????.

?? ????? ??????? ???? ?????? ??? ????? ??????? ?????? ?? ???????? ??? ?? ???? ?? ????? ?????? ?? ?????? ????? ????? ?????? ??????? ?? ????? ?????.

???? ????? ?????? ???? ?? ?? ??????? ?????? ????? ???? ??????.

??? ??????? ?????? ?????? ??????. ???????? ??????? ?????? ??????? ??????? ???? SMN1 ?? ????? ??? ??? ??? SMN2.


3. ????? ????? ??????? ?????

????? ?????? ????? ??????? ?? ?????? ?????? ?????? ??? ??????? ??????? ??????? ?????? ???? ??? ????? ??? ??????? ?????? ???? ?????.

???? ??????? ????????:  ?????? ??? ???????? ??????? ???????? ????????? ??? ?????? ?????? ????? ???????? ?? ?????? ???????? ????? ??????  ??????? ?? ???????? ???????? ??????? ?????? ?????? ???????? ?????? ???????  ?????? ??? ??????? ???????? ??????? ????????  ????? ?????? ?????? ????? ????? ?????????  ????? ?????? ????? ?????? ???? ??? ???? ?? ????????????  ??????? ?? ????????? ????????.

??? ????? ???? ??? ??????? ???????? ???????? ?? ???? ??????. ????? ??????? ?????? ?????? ???? CHOP INTEND ?HFMSE ?RULM? ?????? ???????? ??? ??? ?????? ?????? ???????.

??????? ????? ????? ??????? ?? ???? ?????? ?? ???????? ???????? ???? ??? ?? ???? ????? ????? ???????.


4. ???????? ????????

????? ???????? ???????? ?? ?????? ?????? ?????? ??? ???? ???? ???? ??????: ???? ?? ???????? ?????? ???????? ????? ???????? ??????? ????? ???????? ?????.

??????? ??? ??? ???????? ??? ??????? ???? ???????? ??? ??????? ??????? ????? ???? ????? ?????? ??????? ??? ???? ??????? ?????? ???? ???? ??????? ??????? ??? ????????? ???????. ???????? ??????? ??????? ??????? ???????? ?????? ??????? ?????? ????? ????? ?????.

??????? ??? ???????? ??? ??????? ???? ???????? ?????? ??????? ????? ?????? ??????? ???? ????? ???????? ???????? ?????? ???? ??? ?????. ???????? ????? ?????? ???????? ???????? ???? ????? ?????? ??? ???? ???????.

??????? ??? ???????? ??? ?????? ??????? ??????? ?????? ?????? ?????? ????? ??????? ??????? ??????? ??????? ???????. ????? ?????? ???? ????? ????? ??? ??? ????? ??????.

????? ??????? ????? ?????? ?????? ???????? ????? ????? ???????? ?????? ?? ????? ????? ??????? ??????? ????? ????? ?? ?????? ???????? ??????? ???? ????? ????? ?????? ???????.

??? ?? ?????? ??? ???????? ?? ??????? ??????? ???????? ???? ???? ??? ????? ????.


5. ??????? ??????? ??????? ???????? ???????

???? ??????? ??????? ?? ?????? ?????? ?????? ?????? ???????? ??????? ?????? ??????? ?????? ???? ?????? ????? ????????.

??? ?????? ???????? ????? ???? ????? ??????? ?? ?????? ?????? ?????. ??? ???? ????? ?????? ??????? ??????? ??? ??????? ????????? ???????? ??? ????? ??????? ????? ?????? ?????? ???????.

???? ????? ?? ??????? ??????? ????????? ??????? ??? ????? (TENS) ???? ???????? ????? ????????? ??? ????? ??????? ??????? ?????? ?? ????????? ?????????.

????? ??????? ??????? ????????? ?????? ?????? (NMES) ????? ?????. ???? ????? ?????? ?? ????? ??????? ?????? ?????? ????? ??????? ?? ??????? ???????? ??? ???? ?????? ?????????? ??????? ????????? ?????? ?????? ????????? ??????.

?? ???? ?? ??????? ??? ??????? ???????? ?? ?????? ??????? ??? ??????? ?? ?????? ????????? ??????????? ???? ?? ???? ?????? ?????? ??????. ???? ??? ??? ????????? ?????????? ????? ?????? ??? ???????? ??????? ?? ????? ???????? ???????? ?? ????? ???????.


6. ????? ??????? ???????? ????????

????? ??????? ????????? ????? ???? ?? ?????? ?????? ?????? ???? ?????? ?????? ???? ????? ????????? ???????? ???? ??????? ????? ?????.

??? ?????? ????? ????? ????? ????? ?? ????? ??????? ??? ?????? ??? ????? ?????? ????? ????? ?????? ??????.

????? ??????? ???????? ??????? ?????? ???????? ??????? ????? ?????? ????? ?????? ?????? ??????? ??? ????? ?????? ?????? ??????? ?????? ???????.

??????? ????? ??????? ?????? ?????? ?????? ???????? ??? ???????? ??? ???? ???????. ????? ????? ?? ?????? ??????? ??? ?????? ?????? ?????? ???????? ?? ??????? ???????? ??????? ????????.

???? ????? ??????? ??????? ??????? ??? ??????? ????? ?????? ???????? ?????? ???? ?????? ??????? ????? ????? ?????? ?? ???????.

??? ?????? ?????? ?????? ??? ????? ??? ????? ????????? ?? ?? ???? ?????? ??????? ?????? ?? ?????? ???????? ??????? ???????.


7. ????? ??????? ??? ?????????? ???????? ?????????

????? ???? ???????? ???????? ?????? ?????? ?????? ??????? ??????? ???? ?????? ????????? ?????.

??? ??? ??????? ??????? ?? ???? ????? ??????. ??? ??????? ??????? ????? ?????? ????? ????? ??? ?????? ??????? ??? ?????? ??? ?? ????? ??????? ????? ??????.

???? ???????? ???????? ????? ?????? ?????? ???????? ??????? ??????? ??? ??????? ??????. ???????? ????? ???????? ??????????? ??? ?????? ???????? ??? ??????? ??? ???? ???????.

????? ???????? ????? ????? ????? ???????? ??? ????????? ?????? ???? ??? ????????? ???????. ??? ???? ??? ????? ????? ??? ??? ????? ??????? ???????.

???? ?????? ?????? ?????? ?????? ?????? ?? ??? 5q ????????? (nusinersen) ?????????? (risdiplam) ??????? ???????? ????? ???????? ??????????? ??????????? (onasemnogene abeparvovec) ?????? ????????? ??????????? ???????. ????? ??? ???????? ?????? ??????? ?????? ????? ?? ???? ?????? ??? ?????? ????? ??????? ??? ????? ??????.


8. ????? ????????? ???????

??? ????? ????? ???? ?????? ?????? ??????? ??? ??? ?? ??? ?????? ???? ????? ?????? ?????????? ??????? ???? ?????????? ?????????.

?? ???? ????? ?????? ???? ??????? ?????? ?? ??????? ?? ?????? ?? ???????? ?????? ?? ?????? ?????? ??? ??????.

??? ???? ????? ???? ????? ?? ?????? ?? ?????? ?????? ?? ??? ??????? ???????? ??? ???? ????????? ??????? ???????? ??????? ??? ???????.

????? ??????? ??? ?????? ??? ????? ???? ????? ?????? ????? ??????? ???? ??????.

??? ???? ???? ?????? ???? ?? ????? ???? ????? ?? ?????? ??? ???????? ??? ????? ????? ?? ???????? ??????.

?????? ???????? ????? ??????? ??? ????????? ?????? ???????? ?????.


9. ?????? ?????? ?????? ??????

??? ????? ?? ?????? ????? ??????? ???????? ?? ????? ???? ???? ????? ????????? ?? ???? ???????? ?????? ???????? ??????.

??? ??????? ???????? ???? ????? ?? ????? ????? ????? ????? ??????? ??????? ???? ????? ?????? ?????? ????? ????? ?????? ????????.

????? ????? ?????? ?????? ???????? ??? ?????? ?? ?????? ???????? ?????? ????? ?????? ??????? ??????? ???????? ??????.

??? ???? ?????? ??? ?????? ????? ??????? ??? ???? ???? ??? ?? ???? ??????? ??????.

??? ?? ???? ?????? ?????? ????? ?????? ????????: ??? ?????? ?????? ????? ????????? ??????? ??? ??????? ??????? ?????? ????? ?????.

????? ?????? ????? ?????? ?????? ???????? ????? ????? ??? ????? ????? ?????? ???????? ???????. ?????? ???? ?????? ????? ????? ???????? ??????? ?? ????? ???????.


10. ???????

???? ?????? ?????? ?????? ????? ???? ??? ??????? ??????? ??????? ????????? ??? ???????? ??????? ????????? ????? ????? ????? ??? ????? ?????? ??????? ?????? ????? ?????.

????? ??? ????? ??????? ??? ???????? ???????? ???? ????? ?????? ??? ?????? ??????? ?????? ????? ??????? ??????? ????? ??????.

??? ????? ??? ??????? ????? ??????? ??? ??????? ?? ????????? ????????? ?? ???? ????? ????????? ?? ????? ??????? ?? ??????? ??????? ??????? ???? ???? ????? ??????.

????? ??????. ??????? ???????? ?????? ??????




????? 8. ??? ????????????


??? ????????????


1. ??????? ?????? ?????

??? ???????????? ?? ?????? ?? ??????? ???????? ???? ???? ?????? ?????? ???????? ?????? ?????? ?????? ?? ??????? ?????? ??????? ??? ???? ?? ??????? ??????? ?? ???????.

?? ???? ??????? ??????? ??? ???????? ?????? ???????? ??????? ?? ??????? ??????? ?????. ????? ???? ???????? ??????? ????? ????? ???????? ?????? ?????? ?????? ?????? ?? ?????.

???? ????? ????? ????? ????. ?????? ????? ?????? ??????? CMT1A? ?????? ????? ????? ????? ??? ??? PMP22. ????? ????? ???? ?? ?????? ?? ????? MPZ ?GJB1 ?MFN2 ?????? ??????. ??? ???? ??? ??????? ?????? ?????? ?? ?????? ??????? ?? ??????? ??????? X.

?????? ?????? ??? ???????????? ???????? ???? ???? ????? ??? 2,500 ???. ?????? ?????? ???? ???? ??? 2023? ???? ???? ???????? ??????? ????? ??????????? ??????? ???????? ???????? ???????? ?? ??? 17.7 ???? ??? 100,000 ????. ?????? ?????? ??? ????????? ?????? ????????? ???????? ???????? ??????? ??????? ?????? ??? ???????. ????? ??? ???????? ?? ???? ??????? ??????? ??????? ???????? ??????.


2. ?????? ????????

???? ??????? ?????? ?????? ?? ??????? ?? ????????? ??? ?? ??? ??????? ?? ???? ??? ?? ??? ????? ????? ??????.

?? ?????? ??????? ??? ????? ??????? ????????? ?????? ????? ?????? ?????? ????? ??????? ??????? ??????? ????? (steppage gait)? ??? ???? ???? ???? ?????? ???? ???? ?? ??????? ??? ?? ???? ????? ????? ???? ?????.

?? ????? ???????? ????? ??????? ??? ????? ??????? (pes cavus)? ????? ????? ????? ????????? ???? ??????? ???? ??????. ????? ???? ????? ??????? ??????? ??????? ???? ????? ????????? ???????? ??????.

???? ??? ???? ?????? ??? ???????? ??? ??? ?????? ?? ???? ???????? ??? ???? ??? ????? ?? ?????? ?? ??? ??? ??? ??????. ????? ????????? ??????? ???? ??????.

???? ????? ??????? ???????? ???? ?????? ?? ????? ??????? ???????? ???????? ?? ??????? ???????.

???? ??????? ????? ?????? ??????? ??????? ????????? ??????? ???????? ??????? ???????? ????????.


3. ????? ????? ??????? ?????

????? ????? ???????? ?????? ??????? ?? ??? ???????????? ?? ????? ??????? ?? ????? ?????? ???? ???? ?? ????? ????.

???? ??????? ????????:

????? ?????? ????? ?????? ???????

??????? ?? ??? ??????? ??????? ??????

?????? ??? ????? ??????? ?????? ??????? ??????? ?? ????????

??????? ?? ???? ???????? ???????? ??????? ???????? ??????? ??????

?????? ??? ??? ????? ???????

????? ??? ?????? ??????? ????? ???????? ?????? ??? ???????.

??? ????? ??????? ????????? ?? ????? ????? ??? ??????? ????? ????? ????? ??????? ?????? ?????? ????? ?????? ??? ???? ??????? ???????.

???? ??????? ?????? CMTNS ?CMTES ??????? ????????? ?????? CMTPedS ??? ???????.


4. ???????? ????????

???? ???????? ???????? ??? ?????? ??? ??????? ???????? ??????? ????????? ?????? ???????? ?????? ????? ?????? ????????.

??? ??? ??????? ??????? ?????? ??????? ?????? ????? ?????? ?????? ??????? ????? ??? ???? ??????? ??????? ???????? ???? ????? ??????. ???????? ?????? ????? ??? ?????? ?? ??? ?????? ???? ??? ?????.

??????? ?????? ??????? ?? ?????? ??? ???? ?????? (?? ????? ?????). ???????? ?? ??????? ????? ????? ??????? ?????? ?? ????? ????? ?????? ???????? ?? ?????? ??? ???????.

??????? ?????? ??????? ??????? ???????? ?????? ?????? ??????? ?? ??? ??? ????. ???? ???? ?????? ?????? ??????? ??? ?????? ????? ?????.

???? ????? ?????? ????? ??????? ???????? ??????? ??? ?????? ?????? ??????? ??????? ??? ?????? ????????.

?? ???? ?????? ???????? ??????? ??????? ????? ?????? ??? ?? ??? ??????? ??????? ???????? ?????? ?????? ?????? ??????? ???????. ???? ???? ??? ????? ????? ???? ????? ??????? ????? ?????? ??????? ??????? ??? ???????.


5. ??????? ??????? ??????? ???????? ???????

???? ??????? ??????? ?? ??? ???????????? ?????? ????? ?????? ??????? ???????? ??? ???? ????? ?????? ?? ???? ?????? ?????? ????? ??????? ??? ???????.

??? ?????? ????? ??? ??? ?????? ??? ??? ?????? ??? ?????? ?? ?? ?????? ?????? ????? ??????? ?????????? ?????? ?? ????? ???????.

???? ????? ?? ??????? ??????? ????????? ??????? ??? ????? (TENS) ?? ??? ???????? ?????. ???? ??????? ??? ????? ?????? ??????? ?????? ??????? ??? ?????? ??????? ??????? ????? ??? ????????.

????? ??????? ??????? ????????? ?????? ?????? (NMES) ??? ???? ????? ??????? ????? ???? ??????? ?? ???????. ???? ???? ????? ?????? ?????? ?? ???? ?????? ??????? ???????? ??????. ??? ???? ??? ??????? ????? ????? ???????? ??????? ??????? ???????? ?? ?????.

?? ?????? ???? ????? ??? ???? ??????? ??? ??????? ???????? ?? ?????? ??????? ??? ??????? ?? ?????? ????????? ??????????? ??? ????? ???? ?????. ??????? ????????? ????? ??????? ??????? ???????? ?? ???? ??? ??? ??? ??? ???? ??????? ??? ?????.


6. ????? ??????? ???????? ????????

??????? ???????? ?? ??? ???????????? ????? ?????? ?? ???? ?????.

??? ???? ?????? ??????? ????? ????? ?????? ?????? ??????? ?????? (AFO) ?????? ??? ????? ???? ????? ??????? ?????? ??? ??????.

??? ???? ????? ??????? ???? ??????? ??????? ?????? ????? ????? ??????? ????? ??? ????? ????? ????? ???? ???????. ???? ?????? ??????? ?? ??? ???? ??? ???? ??? ????? ????? ?? ?????.

???? ????? ?? ??????? ??????? ???????? ??????? ???????. ?????? ?????? ??? ????? ??????? ?????? ?????? ?????? ???????? ???????? ????????.

??????? ??? ?????? ????? ?????? ??? ??????? ??????? ????? ????? ?????? ?????? ????? ?????? ?????? ???? ??????? ????????.

??? ????? ??????? ????????? ????? ??????? ??????? ??????? ????? ????? ?? ??????? ??????? ?? ???? ?????? ?????? ?????? ????? ?????.


7. ????? ??????? ??? ?????????? ???????? ?????????

?? ???? ??????? ??????? ?? ??? ????????????? ??? ???????? ?????? ??????? ?????? ????? ??????? ????????. ??? ???? ??????? ?????? ????? ?? ????? ?????? ?????? ?????? ?????.

??? ??? ????????? ???????? ??????? ?? ?????? ?? ??? ?????? ????????? ????? ?????? ?????? ??????? ?????? ????? ??????.

??? ???? ??? ??? ??? ???? ?? ??? ????? ???? ?? ???? ?? ????? ?? ???? ?????? ???? ????? ????? ?????.

????? ????? ?????? ???????? ?????? ??? ???? ??? ???? ????? ?????? ?? ????? ?? ????? ?? ??????? ???????.

??? ?? ????? ?????? ????? ?????? ??? ?????? ????? ?????? ?????? ?????? ??????? ???????? ????? ?? ?????? ????? ?????????? ?????? ?? ???? ????? ????? ????? ????????.


8. ????? ????????? ???????

??? ???? ??? ??? ????? ????? ??????? ??? ?????? ????? ?????? ????? ?????? ?? ?? ????? ???????? ????? ??????.

?? ???? ????????? ???????? ??????? ?????? ?????? ?????????? ?????? ??? ???? ??????? ??? ?? ??????? ?????? ?? ????? ???????.

????? ???? ???????? ???? ????? ??? ??? ????? ?????? ??? ????? ????? ??????? ??? ???? ??? ?????? ?????? ?? ??? ???????.

??? ???? ?????? ?????? ?? ????? ???????? ?????? ????? ?????? ????? ??? ??????. ??????? ???? ????? ?? ?????? ?? ????? ?????? ??????? ????????? ?????? ???? ?????? ??????.

??? ????? ????? ?? ???????? ???? ???? ??????? ?????? ?? ??????? ???????. ???? ??????? ????? ??????? ????????? ????? ?????? ?????? ?????? ??????? ???????? ???? ???????.


9. ?????? ?????? ?????? ??????

????? ???? ??? ???????????? ???? ??????? ??????? ??? ???? ??? ?????? ???? ????? ?????. ??? ????? ?????? ?????? ????? ?????? ?????? ????? ?????? ?? ????? ???????.

??? ?? ????? ??????? ??? ????? ????? ?????? ??? ???? ???????? ???????. ???? ??????? ??????? ?????????? ????? ?????? ?? ???????? ??????.

?????? ?????? ?? ??????? ??????? ????? ????? ???? ?????? ??????? ?? ????? ???? ????? ?? ??????? ???? ????? ???? ??? ??????.

??? ??? ??????? ????? ????? ??????? ???????? ??? ?????? ??? ??????????? ??? ?????? ??? ?????? ?????? ?? ???????.

??? ??? ???????????? ???? ?????? ?? ??????? ????????? ??? ????? ?????? ?????? ????? ?????????? ???????? ??????.


10. ???????

????? ??? ???????????? ??????? ??? ??????? ??????? ????????? ???? ????????? ????????? ??????? ?? ???????.

????? ?????? ??????? ?????? ??????? ?????? ?? ????? ?????? ??????? ??????? ????????? ?? ????? ??????? ??????? ??? ????? ?????? ???????? ?? ??????? ??? ????.

??? ?? ????? ?????? ????? ??????? ????? ??????? ?????? ?????? ???? ??????? ???????? ???????? ???????? ??????. ?????? ????? ???? ????? ?????? ??? ???? ??????? ???????? ????? ??????? ????? ?????? ???????? ??????? ?????????.

????? ??????. ??????? ???????? ?????? ??????




????? 9. ????? ?????? ??????? ???????


????? ?????? ??????? ???????


1. ??????? ?????? ?????

????? ?????? ??????? ??????? ?????? ??? ??????? ??????? ?? ??????? ???????? ????? ?????? ???????? ??????? ??????? ?? ????? ?????? ????? ??????? ???????? ???????? ?????? ?????? ?? ??????? ????????.

???? ??????? ??????? ?????? ???????? ??????? ???????? ??? ???? ???????? ??????? ????? ??????? ???????? ????????.

??????? ??? ??????? ??? ??????? (??????) ???????? ??????? ?? ?????. ??????? ?????? ?????? ?????? ??????? ??????? ????????? ?? ??? ?? ?????? ??????? ?? ???????? ????? ??????.

????? ????? ??????? ?? ????????? ????????? ????? ???????? ?? ????? SPAST (SPG4) ?ATL1 (SPG3A) ?REEP1 (SPG31) ?SPG7. ????? ????? ????? ????? ????? ?????? ?????? ??????? ??????? X.

????? ??????? ????????? ??????? ???? ???????? ???????? ????? ?????? ??????? ??????? ???? 3.6 ???? ??? 100,000 ????. ?????? ??????? ?????? ??????? ???????? ????? SPG4? ???? ?????? ????????? ????????? ?????????.


2. ?????? ????????

?????? ??????? ????? ?? ?????? ???? ??????? ???????? ????????? ?? ?????? ???? ??????? ?????? ?????.

???? ????? ?????? ?? ??? ????????? ??????? ??????? ?????? ????? ?????? ??????? ?? ????? ??????.

???? ?????? ?????? ??????? ??????? ?? ??????? ??? ??? ????????. ??? ???? ?????? ?????? ?? ??????? ??????? ??????? ??? ???? ??????? ?????? ?????? ???????.

???? ?????? ?? ????? ?????? ????? ????? ????????? ??????? ??????? ?????? ???????? ?????? ???????.

?? ?????? ??????? ??? ??????? ?? ?????? ???? ????????? ????????? ??????. ??? ??????? ??????? ??? ?????? ????? ?? ????? ????????? ?????? ??????? ??????????? ???????? ?? ????? ????? ????.

???? ??????? ????? ?????? ???????? ??????? ?????????? ?????? ?????? ?????? ???????? ??????? ?????? ????? ??????? ??????? ????????? ??????? ???????? ????????.


3. ????? ????? ??????? ?????

????? ??????? ?????? ??????? ?? ??? ????? ?? ????? ??????? ???????? ?????? ?????? ?? ?????? ??? ???? ???? ???? ?????? ??????.

???? ??????? ????????:  ?????? ??? ??? ?????? ?????? ?? ????? ????? ??????? ????????  ??????? ?? ???????? ???????? ????????? ??? ???????? ????????  ????? ?????? ???????? ????? ??????  ????? ???????? ????????  ?????? ??? ?????? ??? ?????? ??????? ????? ??????? ??????? ????? ???????  ????? ??? ??????.

??? ????? ???????? ??? ?????? ?? ??? ???? ??????? ?? ?????? ?????? ???? ?? ??????? ???????. ??? ??? ?????? ???? ?????? ??????? ?????? ??? ??????? ?????? ??? ?????? ??? ????? ??????.

??????? ??????? ???????? ????? ????? ?????? (MAS)? ?????? ????? ????? ?????? ??????? (SPRS)? ??????? ????? ?????? ???? ?????? ??????? ?????? ?????? ??????? (TUG).


4. ???????? ????????

???? ???????? ???????? ?? ????? ?????? ??????? ??????? ??? ?????? ??? ???? ??????? ?????? ??????? ???????? ?????? ????? ?????? ?????? ?? ??????.

??????? ??????? ???????? ?????? ????? ????? ??????? ??????? ??????? ?????? ??????? ??? ??????? ??????? ??????? ??????? ???????? ?????? ??????. ?????? ??????? ??? ????? ?????? ?? ?????? ?????.

???? ?????? ?????? ???? ????? ???? ??? ????? ??????? ??? ?????? ??? ????? ????? ?????? ????? ????.

???? ????? ????? ????? ??? ?????? ???? ????? ????????? ?????. ???????? ??????????? ?? ???????? ?? ????? ????? ?????? ???? ????? ??? ??????.

????? ???? ??????? ??????? ??????? ??????? ?????? ?????? ?????? ????? ??????? ????? ?????? ?? ????????? ??????? ?????? ???????. ????? ??????? ??????? ??????? ??????? ??????? ?????? ?????? ??? ??????.

??? ????? ???????? ??? ???? ?????? ?????? ??????. ??????? ????? ?????? ?? ????? ???????? ?? ????? ?????? ??? ??????? ?????? ??? ?????.


5. ??????? ??????? ??????? ???????? ???????

???? ??????? ?? ????? ?????? ??????? ??????? ????? ?????? ?????? ???????? ?????? ????????? ???????? ??? ???? ?? ???????? ????????.

?????? ???????? ??????? ???? ?? ???? ??? ????? ???????? ?? ???? ???????. ??? ???? ????? ?????? ???????? ??????? ??????? ???????? ??????? ????? ??? ??????.

???? ??????? ??????? ????????? ??????? ??? ????? (TENS) ?? ??? ???????? ?????. ?????? ?? ??????? ????????? ?????? ?????? (NMES) ?? ??????? ????????? ??????? (FES) ????? ?????? ??? ???? ??? ??? ????? ????? ?????? ????? ????? ?????.

?? ???? ??????? ????????? ????? ??????? ?????? ???????? ???? ??????? ???? ?????? ?? ????? ?????? ??? ????? ????? ??????.

?? ???? ???? ??????? ??? ??????? ???????? ?? ?????? ??????? ??? ??????? ?? ?????? ????????? ??????????? ??? ????? ???? ?????. ?????? ????????? ?????? ??????? ????????? ?????? ?????? ??????? ????????.


6. ????? ??????? ???????? ????????

????? ???? ???????? ????????? ?????? ?? ??? ????? ???????? ????? ?????? ????? ???? ????? ?????? ????? ???????? ???????? ?? ??????? ????????.

???? ??????? ????? ????? ?????? ?????? (AFO) ??? ?????? ??? ????? ?? ????? ??????? ????? ?????. ??????? ??????? ??? ??????? ??? ?????? ?????? ?????? ?????? ????? ??????.

??? ???? ???? ????? ??? ?????? ??????? ????? ????????? ?????? ?? ????? ??????. ???? ???????? ?????? ?? ?????? ??? ??????? ????? ?? ????? ???? ????? ?????.

???? ????? ??????? ??????? ??????? ??? ?????? ?? ?????? ????????? ????? ?????? ????? ??????? ????????? ??? ?????? ????????.

?? ????? ???????? ???????? ??????? ??????? ????????. ?????? ???? ?????? ??????? ??? ????? ??????? ?????? ?????? ?????? ???????? ??????? ??????? ?? ????????? ??????.


7. ????? ??????? ??? ?????????? ???????? ?????????

?? ??????? ??????? ?? ????? ?????? ??????? ???????? ????? ???????? ?????? SPG11? ????? ????? ????? ????? ????? ?????? ?? ?????? ??? ??? ?? ????? ?????? ??? ???? ????? ?? ????? ??????? ?????? ??????? ?????? ?? ??????? ????? ?????? ?????? ???????.

???? ?????? ????? ??????? ?? ???????? ???????? ??????? ???? ?????? ??? ?????? ????? ?????? ?? ??????? ?????? ?? ??? ?????.

??? ???? ??? ???????? ???? ????? ??????? ??????? ???????. ???????? ???????? ???????? ??????? ???? ?????? ??????? ??? ???? ???????.

???? ??????? ???????? ?????????? ?????? ???? ????? ?????? ?????? ?????? ?????? ??????. ????? ????? ?? ??? ????? ??????????? ??? ????? ?????? ?????? ????????? ??? ????? ?????????? ???? ?????? ??? ?????? ?????? ?????? ??????.

????? ??? ?????? ?????? ???????? ?????? ??????? ??? ?????? ??????? ?????? ?? ???? ???? ??????.

?? ??????? ???????? ??? ?? ????? ?????? ????? ??????? ????? ????? ????????? ?????? ??????? ????????? ?????? ???????? ????????.


8. ????? ????????? ???????

??? ????? ????? ???????? ?????? ?????? ??????? ???????? ??? ???? ??????? ??????? ???????? ???????? ??????? ??????? ????????.

????? ???????? ???? ????? ??? ??? ????? ????? ??? ?????? ???????? ????????? ????? ?? ??????? ?? ???????? ??????.

??? ????? ????? ??????? ????? ????? ????? ??????? ???? ???????? ???????? ????? ???????? ?????.

??? ??? ???? ??? ?????? ?????? ????? ??? ????. ???? ????? ????? ??????????? ?? ????? ?????? ?????? ??????? ????? ????? ????? ???? ?????? ??? ?????? ??????.

?????? ???? ??? ???? ???? ??????? ?? ?????? ??? ???? ?? ????? ????? ?? ?????? ????? ???? ?????? ???????? ??? ???? ???.


9. ?????? ?????? ?????? ??????

????? ?????? ??????? ??? ???? ???? ?????? ?? ??????? ??? ?????? ???? ??????? ?????? ???????? ????????.

????? ????? ?????? ??? ?????? ????? ??? ?????? ??? ???????? ???? ??????? ??? ??????? ??????.

??? ???? ???? ???? ????? ?? ????? ???? ?????? ?????? ?? ?????? ????? ??? ????? ??????? ??? ???????? ???????.

????? ?????? ?????? ?????? ?????? ??? ?????? ??? ?????????? ???????? ????? ?? ???? ??????? ???? ?????? ??????? ????? ??? ??? ????.

??? ????? ?????? ??????? ??? ???? ???? ?????? ?? ???????? ??????? ??????? ?? ???? ????? ?? ??????.

????? ????????? ???????? ?????? ???????? ?? ?????? ??????? ??????? ?????? ???? ???????.


10. ???????

????? ?????? ??????? ??????? ?????? ?? ??????? ???????? ???? ???????? ?????? ??????? ???? ?? ?????? ?????? ??????? ???????? ?? ??????? ????????.

???? ?????? ????? ??????? ?? ????? ?????? ??? ????? ????? ??? ??? ???? ??????? ?????? ???????? ??? ?????? ?????? ?????? ?????? ???????.

?? ????? ???????? ??????? ?????? ??????? ?????? ?????? ????? ?? ????? ??? ?? ??? ??????? ??? ????? ????? ????? ??????? ????? ?????? ??? ???? ??????? ???????.

????? ??????. ??????? ???????? ?????? ??????




????? 10. ??? ????????


??? ????????


1. ??????? ?????? ?????

??? ???????? ??? ????? ???? ????? ????? ?????? ?????? ?? ????? ???????? ?????? ???????? ??????? ?? ????? ?????? ??????? ?????? ??????? ???? ?? ??????? ????????.

?? ???? ??????? ???? ????? ?? ???? ???? ?? ??????? GAA ?? ????? ??? FXN ??????? ??? ?????? ??????. ????? ??? ??? ??? ?????? ??????????? ??????? ???????? ?????????????. ???? ??????? ???? ?????.

?? ??????? ??? ?????? ????????? ?? ?????? ?? ???? ???????? ??????? ?????? ??? ???????? ???? 0.51.8 ???? ??? 100,000 ???? ???? ???????? ?????????? ?????? ???????? ????? ?????? ??? ???????.

???? ????? ???? ?? ??????? ?? ????????? ?? ???? ????? ???? ?? ?? ??????. ??????? ?? ????? ???? ?????????? ??????? ??????? ????? ???????? ?????.


2. ?????? ????????

???? ??????? ?? ????? ???????? ?? ?????? ????? ??????? ??????? ???? ?????? ????? ?????? ??????.

???? ?????? ????? ??????? ???? ?????? ?? ????? ????? ??? ????????. ???? ?????? ????? ?? ???????? ?????? ???? ?????? ????? ?????? ??????? ???????.

???? ????? ??????? ??????? ????? ?????? ???????? ??????? ?????? ??? ?????? ??????? ????????? ??? ????? ??????? ????????. ?????? ???? ??? ???? ?????? ??? ????? ???? ?????? ??? ???????? ??? ??????.

?? ???? ????? ???? ??? ????? ??? ?????? ??????? ?????? ???? ?????? ?????? ??? ????? ??????. ??????? ?? ???? ????????? ??????? ?? ??????? ???????? ?? ?????? ???? ?????? ????? ?????.

???? ????? ????? ???????? ??? ?? ??? ????? ??????? (pes cavus)? ?? ??????? ???????. ??? ???? ?????? ???? ????? ??????? ??????? ????? ?????? ????????? ????? ?????? ???????? ????????????.

??????? ??????? ?????? ??????? ??????? ???? FXN? ?? ??????? ???????? ????? ??????? GAA.


3. ????? ????? ??????? ?????

???? ?????????? ????? ??????? ??? ?????? ??? ??????? ?????? ??????? ??????? ?????????? ?????? ?? ?????? ????????? ???????? ?? ????? ????.

???? ??????? ????????:  ????? ??????? ???? ??????? ?????????  ?????? ??? ?????? ??? ?????? ?????? ?????? ????? ????? ??????  ?????? ??? ??????? ??????? ??????? ????????  ??????? ?? ?????? ??????????  ??????? ?? ???????? ???????? ?????? ???????  ????? ??????? ??????? ?? ????? ????????  ?????? ??? ?????? ??? ?????? ?? ?????? ???? ?????? ?????? ???????.

??????? ???????? ????????? ???? ????? ?????? ????? (SARA)? ?????? ????? ??? ???????? ?????? (mFARS)? ??????????? ???????? ????? ????????.

??? ????? ??? ??? ??? ?????? ?? ????? ???? ?????? ??? ????? ?????? ??????? ??????? ??????? ???????? ??????? ??????????.


4. ???????? ????????

????? ????? ??????? ?????? ??? ?????? ??????? ???????? ?????????? ??????? ?????? ?????.

?? ??????? ??????? ??????? ????? ????? ??? ?????? ??? ??? ???? ?????? ????? ?? ?????? ?????? ??????? ????? ??????? ????? ???? ????? ?????? ???????? ????????.

???? ????? ??????? ?? ????? ?????? ?? ????? ???????? ?????? ?????? ????? ???? ?????. ??? ????? ????? ?????? ??? ?????? ?????? ?????? ??? ???????? ???????.

?????? ???????? ??? ????? ??????? ?????? ????? ??? ?????? ??????? ??????? ??????? ????????? ????? ?????? ?????????? ??????? ??????? ??????. ?????? ????? ???????? ??? ??? ??????.

??? ????? ?????? ??? ????? ??????? ???? ????? ??????? ??? ?????? ?????? ?????? ???? ??? ????? ????????? ??? ?????? ??????? ??? ??????? ???????? ??????.

???? ????? ?????? ??????? ????? ????? ????? ?????? ????? ??? ????? ????? ?????. ?????? ??? ??????? ???? ?????? ????? ?????? ?? ???? ?????????.


5. ??????? ??????? ??????? ???????? ???????

???? ??????? ??????? ?? ??? ???????? ?????? ???????? ?????? ??????? ?????? ?? ???? ?????? ?? ?????? ?????? ?? ???????? ?????????.

??? ?????? ???? ?????? ?? ???? ??????? ???? ??????? ????????? ??? ????? ?? ??? ??? ??????? ?????? ???????.

???? ????? ?? ??????? ????????? ??????? ??? ????? (TENS) ??? ???? ???????? ??? ?????? ??? ????? ?????? ????? ?????? ?????????.

?? ???? ??????? ????????? ?????? ?????? (NMES) ????? ??????? ?????? ?????. ?????? ???????? ????????? ????? ????? ?????? ??????? ??????.

????? ?????? ??????? ?????? ?????? ??????? ?????? ???????? ??????? ??????? ?????? ?? ????? ???????. ??? ???? ???? ????? ??? ?? ?????? ???????? ??? ??????? ?? ?????? ??? ??????? ?? ???????? ??????????? ???? ???? ??? ????????.


6. ????? ??????? ???????? ????????

???? ????? ????? ??????? ?? ????????? ????????? ??????? ???? ????????.

???? ????? ????? ??? ????? ?????? ?????? ???????? ??? ????? ???????? ?? ???? ???? ????? ?????? ?????? ?????? ??????.

?????? ????? ????? ?????? ????? ??? ???? ?????? ?? ????? ???? ??????? ???? ??????. ?????? ????? ??? ???????? ??? ??? ???? ?????? ??? ??????.

?? ????? ?????? ????? ?????? ?? ????? ??? ?????? ??? ??????? ?? ?????? ??? ???? ????? ?? ??? ????? ????? ???? ?????.

???? ????? ??????? ??????? ????? ????? ??????? ?????? ????? ?????? ???????? ???????? ??? ???? ??? ????? ??? ?????? ???????.

??? ????? ?? ??????? ??????? ?????? ???? ????? ????? ???? ??? ???????? ?? ???? ????? ????? ??????? ???????.


7. ????? ??????? ??? ?????????? ???????? ?????????

????????? ??????? ????? ???? ?? ??? ????????. ??? ??? ?????? ???? ????? ??????? ????????? ??? ????? ?? ???? ????? ??????.

????? ???????? ??????? ?? ????? ????? ???????? ????? (ECG) ?????? ??? ????? ??? ??????? ???? ????? ??? ????? ??????. ???? ???? ????? ????? ???? ????? ????? ???? ???????? ???????.

????? ??? ??? ?????? ??????? ????????????? ????? ?????? ??? ???? ?HbA1c ???????. ???? ?????? ??? ??????? ???? ????? ?????? ?????? ?????? ?? ??????? ????? ??????.

????? ??? ?????? ????? ????? ????? ???? ????? ???? ?????? ???????? ??????????? ????? ???????.

???????? ????? ????? ???? ?? ??? ????????. ??? ???? ???????? ???? ????? ??? ????? ??? 98% ?? ?????? ????? ????? ?????. ????? ????????? ?????? ??????? ???? ???? ??? ???? ?????? ????? ?????. ???? ????? ????? ????? ??????? ??? ?? ???? ????? ?????. ???? ???????? ?????????? ?????? ?????? ????? ??? ??? ?????? ??? ??????? ??????? ?? ?????? ???????? ????? ??????.

?? ??????? ???????? ??? ?????? ?????? ?????? ????????? ??????? ????????? ????? ??????? ??? ??? ?????.

???? ???? ??????? ?? ?????? ??????? ?????? ????? ?????? ?? ?????? ????? ???????? ?? ?????? ??????????? ???????? ?????? ??????? ?? ????? ??????.


8. ????? ????????? ???????

????? ?????? ???????? ??????? ??????? ??????? ???? ?????? ??????? ????? ?????.

?? ???? ????? ?????? ????? ??? ??? ????? ?????? ??? ?????? ??????. ???? ???? ??? ???? ??? ???? ???? ???? ????? ????? ????? ?????? ??? ???? ??? ?????.

?? ????? ?????? ???? ????? ?? ???????? ????? ?? ?????? ???? ?????? ????? ??? ?????? ?????? ??? ????? ????.

?????? ???? ??? ???? ?? ????? ?? ??? ??? ???? ?? ????? ????? ?????? ????? ????? ????? ?????? ????? ???.

??? ???? ??? ????? ??????? ?? ??????? ??? ???? ????????? ??????? ????????? ???? ???? ??????? ?????????? ??????.


9. ?????? ?????? ?????? ??????

????? ?? ????? ?????? ????? ??????? ??????? ?????? ?????? ????? ??????? ??????? ??? ?????? ?????? ??????.

??? ????? ??? ?????? ?? ?????? ?????? ????? ???? ???????? ???? ??? ???? ?????? ????? ????? ?? ??????? ???????.

????? ???? ????? ??????? ?????? ?? ????? ?????? ????? ???????? ??? ?????? ?? ????? ??????? ??? ?????? ????? ????????.

????? ?????? ?????? ???????? ??? ???? ?????? ????? ?????? ????? ????? ?????? ?????? ????? ???????? ??????? ????????.

???? ???????? ???????? ??? ???? ??????? ????? ????? ????? ?????? ?????? ?? ??????????? ????? ?????? ????? ??????? ?? ????? ???????.

????? ????????? ???????? ?????? ?????? ?????? ?? ?????? ??? ??????? ?????? ???????.


10. ???????

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????? ?????? ????? ??????? ????? ?? ????? ????? ??? ????? ??????? ???????? ?????? ???????? ????????? ??????? ????????.

??????? ??????? ??????? ????? ??????? ?? ?????? ??? ????????? ?????? ???????? ?????? ????? ?????? ??? ???????? ?? ?????? ???????.

????? ??????. ??????? ???????? ?????? ??????




????? 11. ????? ????? ???????? (??????? ???????)


????? ????? ???????? (??????? ???????)


1. ??????? ?????? ?????

????? ????? ???????? ??? ????? ???? ????? ???????? ????? ????????? ????? ?????? ???? ??????? ?????? ???????? ??????? ?????? ?????????? ??????? ???????? ???????.

???? ????? ?? ?????? ????? ?? ???? ????? ??? ATM ??????? ??? ?????? ?????? ???. ????? ???????? ???? ????? ??? ????? ?? ?????? ??? ??? ????? ?????? ?????? ??????? ?????? ??. ???? ??????? ???? ?????.

????? ????????? ???????? ????????? ???? ???? ???? ????? ??? ???? ????? ??? 40,000100,000 ???? ?? ????? ?????? ??? ?? ??? ????????? ????????.

??????? ??? ????? ????????? ?? ??????? ??????? ??????? ?????? ?????????? ???????? ???????? ???????? ??? ?????? ????? ?? ??? ??????.


2. ?????? ????????

???? ???????? ?????? ????? ????? ???????? ????????? ???? ?? ??????? ???????? ????? ???? ????? ?????? ?????? ????? ??????.

???? ??????? ??????? ?????? ??? ??????? ???? ????? ???? ????? ?????? ??????? ??????? ?????? ?????? ???????? ????????. ??? ???? ????? ?? ???? ??? ?????? ???? ?????? ?????? ???????? ??????? ????????? ?????? ???????.

????? ???????? ????? ??????? ????? ??? ???? ??????? ??????? ???????? ???? ???? ?????? ?? ?????? ????? ??????. ??? ???? ??? ??? ??????? ???????.

?????? ??? ??? ?????? ???? ?????? ?????? ????? ?????? ????? ????? ?? ????. ???????? ??? ?????????? ???? ?????? ??????? ???????? ??? ??????? ??????.

????? ?????????? ???????? ?? ????? ???????? ??????? ?????? ???? ?????? ???????. ??? ???? ??????? ????? ????? ????? ????????? ??????? ??????.

????? ??????? ??? ??????? ???????? ?????? ??????? ????? ???? ?????????? (AFP) ?????? ??????? ??????? ???? ATM. ????? ?????? AFP ????? ?????? ???? ??? ??????? ???????? ???????.


3. ????? ????? ??????? ?????

???? ?????? ????? ??????? ??? ?????? ??? ??????? ???????? ?????? ?? ?????? ??????? ???????? ????????? ????????.

???? ??????? ????????:  ?????? ??? ?????? ?????? ????? ???????  ????? ?????? ?????? ??????? ????????  ?????? ??? ?????? ?????? ??????? ???????? ????????  ??????? ?? ???????? ?????????? ????????? ?????????  ????? ??? ???????  ??? ?????? ?????? ?????? ??????? ?????????  ??????? ?? ??????? ???????? ????????? ?????.

??? ????? ???????? ?? ????? ?????? ??? ??? ??? ?????? ?? ????? ???? ?????? ?????? ?????? ????????? ???????? ?????? ???????? ????????.

???? ??????? ?????? ?????? ????? SARA? ??????? ???????? ??? ????? ??????? ??????? ?????? ??????? ??????? ??????? ?????.


4. ???????? ????????

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?????? ???????? ??? ????? ??????? ????? ???????? ????? ?????? ????? ??????? ??????? ?????? ????? ?? ???????? ???????.

?? ???? ?????????? ??????? ????? ??????? ??? ???? ?????? ????????? ??????? ??????? ??? ????? ??????? ??????? ???????? ?? ????????.

????? ?????? ????? ??????? ??????? ?? ?????? ?????? ??????. ??? ????? ??????? ??????? ??????? ????? ????? ?????? ?? ??????? ???????? ?? ??????? ?????.

??? ?????? ???? ??????? ?????? ????? ??? ?????? ??????? ??? ???? ?? ?????? ??????? ????? ???? ????? ?????? ????? ?????.


5. ??????? ??????? ??????? ???????? ???????

???? ??????? ??????? ?????? ???????? ?????? ??????? ?????? ???? ?????? ?????? ???? ?? ????? ??????? ?????? ?? ??????? ???????? ???????.

??? ?????? ???????? ???? ???? ?? ?????? ?? ?????? ??? ?????? ??????? ???????? ??????? ??? ??? ???? ?????.

???? ????? ?? ??????? ????????? ??????? ??? ????? (TENS) ???? ???????? ?????? ???? ??? ????? ????? ???????? ?????? ???????.

??? ??????? ????????? ??????? ?????? ????? ?? ?????? ????? ???????? ??? ????? ???????? ??? ??? ???? ????????? ?????? ??????.

?? ???? ???? ?????? ???????? ??? ??????? ?? ?????? ??? ??????? ?? ???????? ??????????? ??? ????? ???? ?????. ???? ??? ?? ????? ???????? ??????? ??? ????? ???? ??????? ?????????? ????????.

????? ??????? ??? ??????? ?????? ??????? ??????? ??????? ????????? ????????? ????????? ?????? ??? ????? ?????? ????? ?????? ???????? ??????.


6. ????? ??????? ???????? ????????

?? ???? ??????? ???????? ?? ?????? ?????? ?? ???? ????? ????????? ??? ???????? ??????? ?????? ?????? ?????? ?????.

??????? ??? ?????? ????? ???? ????? ??????? ??????? ?????? ?????? ????? ?????. ??????? ????? ????? ?????? ?????? ??? ????? ?????? ?????? ?????? ???????. ???? ?? ??????? ?????? ????? ?? ????? ??????? ??????? ????.

?? ????? ??? ?????? ?? ???? ??????? ???????? ??????. ?????? ???????? ?? ????? ??????? ??? ??????? ?????? ?????? ?? ?????? ???????? ???????? ???????.

??? ?????? ??? ????? ?????? ??????? ????? ???? ?????? ????? ?????? ?????? ???????.

????? ???? ??????? ??????? ???????? ????????? ??????? ??? ????? ???? ?????? ?????? ??????? ??????? ???????? ???????? ???????? ???????.


7. ????? ??????? ??? ?????????? ???????? ?????????

?? ???? ???????? ?? ????? ????? ???????? ?????? ??? ??????? ?? ????? ?????? ??????? ???????.

?? ???? ?????? ???????? ???? ???? ?????? ?????????? ?????? ??? ???? ??????? ?????? ????? ???????.

???? ????? ??????? ??????? ????? ?????? ?????? ???????? ??? ?????? ????? ??????? ???????? ??????? ??????? ????? ?????? ?????? ????????? ???????. ???????? ??? ??????? ????? ?????? ???????? ??? ??????.

?? ???? ??????? ???????? ?????? ???????? ?????????????? ???????? ???????? ?? ?????? ??? ??????????? ???????.

?? ?????? ??? ????? ?????? ???????? ?? ????? ????? ???????? ????? ??? ????????? ???????? ??????? ?? ????????? ??????. ??? ???? ????????? ??? ???? ?????? ???? ?????? ????? ???????? ?????? ??????? ?? ????? ????? ?????? ??????? ???????? ?????? ????? ??? ?? ???? ?????? ?? ??????. ???? ???? ??????? ????? ????? ??? ????? ?????? ????? ?????? ?????? ???? ?????? ?????? ????? ???????.

????? ????? ??? ??????? ???????? ??? ???? ??????? ????????? ?????? ????? ????? ????. ?????? ?????? ??? ?????? ??????.

???? ?????? ????? ????? ??????? ?? ????? ???????? ???????? ?????? ???????? ???? ??????? ??????? ??????? ????? ?????? ?????? ????? ????????? ??? ???? ?? ???? ??? ?????.


8. ????? ????????? ???????

????? ????? ??????? ?? ????? ????? ???????? ?? ????? ???????? ??????? ??????.

??????? ?? ???? ?????? ??????? ???????? ??????? ???????? ???? ????? ?????? ?? ?????? ??????? ??????? ????? ??????? ???????? ???????? ??? ??????? ???????? ??????? ??????????. ???? ??? ????? ???????? ??????? ??????? ????? ?????? ????? ????? ?? ????? ?????? ??? ???? ??.

????? ?????? ???????? ???? ???? ??? ???? ???? ?????? ?????.

??? ???? ??? ????? ????? ??? ???? ???????? ??? ???????? ????? ?????? ??????. ??????? ?????? ?????? ?? ????? ?? ????? ??????? ????? ????? ???????? ??????.

?? ???? ????? ?????? ????? ??????? ?? ??? ?????? ??? ????? ??????? ????????.

??? ???? ???????? ??? ?????? ?? ???? ????? ??????? ?????? ??? ??????? ??? ???? ????? ????? ?? ??? ????? ???? ??? ????????? ??????.


9. ?????? ?????? ?????? ??????

??? ????? ?????? ?? ????? ??????? ?? ????? ????? ???????? ????? ?? ????? ??? ??? ?????????? ???????? ?? ????? ???? ???????? ??????? ????????.

????? ????? ??????? ???????? ??????? ???????? ???? ?????? ????? ????? ????? ?????.

?? ????? ????? ?????? ?? ????? ??????? ??????? ?? ??????? ??????? ??? ???????? ???????? ?? ??????? ???????? ??????? ???????? ??????? ?????.

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??? ????? ?????? ??????? ??? ????? ???????? ???????? ?????? ???????? ??????? ??? ??????.

????? ?????? ?????????? ???????? ?????? ?? ?????? ??? ??????? ?????? ???????.


10. ???????

????? ????? ???????? ??? ????? ????? ??????? ?????? ??? ?????????? ??????? ???????? ?? ??? ??????? ?????????? ???????? ??????? ??? ??????? ????????.

??? ?? ????? ?????????? ????? ??????? ????? ?????? ?????? ?????? ??????? ????? ?????? ??????? ??????? ???????? ????????? ???????.

????? ?????? ???????? ?????? ??????? ????? ?? ?????? ??? ??????? ??????? ???????? ?? ????????? ?????? ?????? ?? ???? ??? ???? ?? ???????? ?? ?????? ???????.

????? ??????. ??????? ???????? ?????? ??????




????? 12. ??? ????????


??? ????????


1. ??????? ?????? ?????

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